Abstract: In order to determine the prevalence of extrapulmonary tuberculosis in children in Zahedan, this study was conducted. In this cross-sectional, retrospective study, all patients aged less than 18 years with tuberculosis disease were evaluated. Then prevalence of extrapulmonary tuberculosis in children determined. This study showed that extrapulmonary TB form 23% of all tuberculosis cases. Tuberculosis lymphadenitis was the most prevalent form of extrapulmonary TB (8%) and pericarditis was the less than other forms (2%). Extrapulmonary tuberculosis is more prevalent in Southeast of Iran than other region in this country.